عنوان
پدید آورنده
موضوع
رده
کتابخانه
محل استقرار
NATIONAL BIBLIOGRAPHY NUMBER
Number
LA33n0k26j
LANGUAGE OF THE ITEM
.Language of Text, Soundtrack etc
انگلیسی
TITLE AND STATEMENT OF RESPONSIBILITY
Title Proper
Secondary bilateral striopallidodentate calcinosis associated with generalized pustular psoriasis (Von Zumbusch)
General Material Designation
[Article]
First Statement of Responsibility
Pacheco, David; Travassos, Ana Rita; Antunes, Joana; Marques, Manuel Sacramento; Filipe, Paulo; Silva, Raquel
SUMMARY OR ABSTRACT
Text of Note
Bilateral striopallidodentate calcinosis (BSPDC) mentioned in the literature as Fahr's disease (a misnomer), is characterized by symmetrical and bilateral intracerebral calcifications located in the basal ganglia with or without deposits in the dentate nucleus, thalamus, and white matter. This entity is usually asymptomatic but may be manifested by neurological symptoms. Idiopathic BSPDC can occur either as sporadic or autosomal dominant familial forms. Secondary presentations of BSPDC are associated with infections, neoplastic diseases, toxicological or traumatic factors, and metabolic disorders. We describe a case of generalized pustular psoriasis associated with secondary BSPDC owing to pseudohypoparathyroidism. Laboratory tests revealed hypocalcemia, hyperphosphatemia, and a normal serum level of parathormone. The correction of the phosphorus-calcium metabolism disorder produced clinical improvement.
SET
Date of Publication
2013
Title
Dermatology Online Journal
Volume Number
19/6
PERSONAL NAME - PRIMARY RESPONSIBILITY
Entry Element
Pacheco, David; Travassos, Ana Rita; Antunes, Joana; Marques, Manuel Sacramento; Filipe, Paulo; Silva, Raquel
ELECTRONIC LOCATION AND ACCESS
Electronic name
مطالعه متن کتاب [Article]
275578
a
Y
