Analytical Chemistry, Biochemistry and Diagnosis of the Organic Acidurias
by R.A. Chalmers, A.M. Lawson.
Dordrecht
Springer Netherlands
1982
1 Introduction --;References to Preface and Chapter 1 --;I: Methods --;2 Extraction of Organic Acids from Physiological Fluids --;3 Derivatives of Organic Acids --;4 Separation, Quantification and Identification --;5 Gas Chromatography-Mass Spectrometry --;6 Volatile Carboxylic Acids --;References to Part I --;II: Organic Acids in Physiological Fluids from Normal Subjects --;7 Organic Acids in Blood and Urine from Normal Healthy Adults and Children --;8 Organic Acids in Physiological Fluids Other than Urine and Blood --;References to Part II --;III: Organic Acids in Human Metabolic Diseases (The Organic Acidurias) --;9 Organic Acids in the Study of Metabolic Diseases --;10 Disorders of Branched-Chain Amino Acid Metabolism --;11 Disorders of Propionate and Methylmalonate Metabolism --;12 Specific Causes of Congenital Keto Acidosis in Infants --;13 Disorders of l-Lysine Metabolism --;14 The Dicarboxylic Acidurias --;15 Congenital Lactic Acidurias and Disorders of Pyruvate Metabolism --;16 Organic Acidurias due to Disorders in Other Metabolic Pathways --;Appendix of Mass-Spectrometric and Gas-Chromatographic Data.
The writing of this book was prompted by the need for a comprehensive of current data on organic acids suitable for both newcomers and collection established researchers in this field.